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Autoimmune Inner Ear Disease

What Is Autoimmune Inner Ear Disease

Autoimmune Inner Ear Disease (AIED) is a rare condition where the body’s immune system mistakenly attacks the inner ear, as if fighting off an infection. Although uncommon—responsible for only about 1% of all hearing loss cases—Dr. Sperling has extensive experience diagnosing and treating this disorder.

What Are The Symptoms?

AIED often mimics Meniere’s disease. Patients typically experience progressive or fluctuating hearing loss in both ears. Other symptoms may include tinnitus (ringing in the ears) and aural fullness (a sensation of pressure in the ear). Diagnosis is made through a combination of clinical evaluation and blood tests that are performed in-office.

How Is It Treated?

Prednisone, a steroid, is commonly used to suppress the immune response. Today, many patients benefit from intratympanic steroid injections, which deliver medication directly into the ear. This method provides high local effectiveness while reducing the risk of systemic side effects. The procedure is quick, painless, and performed under mild anesthesia in the office. In some cases, alternative devices may also be used to administer the treatment.